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KMID : 0357920120460060583
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Korean Journal of Pathology
2012 Volume.46 No. 6 p.583 ~ p.586
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Rosai-Dorfman Disease: Report of a Case Associated with IgG4-Related Sclerotic Lesions
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Park Bong-Hee
Son Da-Hye
Kim Myung-Hwan
Shim Tae-Sun
Lee Hee-Jin
Huh Joo-Ryung
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Abstract
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We describe a rare case of sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease) associated with a six-year history of autoimmune pancreatitis, which was controlled by steroid treatment. The patient presented with multiple, cervical and thoracic lymphadenopathy and abnormal, nodular opacities in the lung. Histologically, Rosai-Dorfman disease with numerous IgG4-positive cells was identified in a subcutaneous lymph node in the patient’s left forearm. The patient recovered uneventfully with steroid treatment.
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KEYWORD
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Rosai-Dorfman disease, Histiocytosis, sinus, Immunoglobulin G4
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